Gender/ Age (years)

Number of infusions of NTZ

Hemoglobin

Management

Treatment switch

Midaglia 2012 [5]

F/50

1

5.4 g/dL

Transfusions, Intravenous immunoglobulin and steroids

NA

Simone 2014 [6]

F/51

34

7.3 g/dL

Transfusions, Discontinued NTZ

NA

Seibert 2015 [7]

F/49

15

7.4 g/dL

3 monthly blood transfusions

Discontinued NTZ

NA

Our Case

M/18

16

3.2 g/dL

Transfusions,

Discontinued NTZ

Rituximab