n = 36

Age (year)

50.8 ± 19.0

Age range (year)

19 - 82

Diagnosis age (year)

43.4 ± 17.2

Sex

Male

25 (69.4%)

Female

11 (30.6%)

Diagnosis length (year)

6 (1 - 20)

Family history

29 (80.5%)

Accompanying disease

HT

27 (75.0%)

CKD

21 (58.3)

Liver Cyst

23 (63.9%)

Intracranial aneurysm

1 (%2.8)

Valve disease

6 (16.7%)

CAH

5 (13.9%)

LVH

18 (50%)

DM

5 (13.9%)

Nephrolithiasis

8 (22.2%)

Macroscopic hematuria

6 (16.7%)

Proteinuria

11 (30.6%)

CKD length (year)

6 (3 - 15)

Hemodialysis

7 (19.4%)

Renal transplantation

3 (8.3%)

Antihypertensive medication used

ARB

9 (25%)

ACE-I

8 (22.2%)

ARB + Calcium channel blocker

4 (11.1%)

ARB + Beta blocker

2 (5.6%)

ACE-I + Calcium Channel blocker

3 (8.3%)

ACE-I + Beta blocker

1 (2.8%)

None

9 (25.0%)