| Localization | Symptoms |
| Head-neck | Asymptomatic mass, may mimick enlarged lymph node |
| Orbit | Proptosis, chemosis, ocular paralysis, eyelid mass |
| Nasopharynx | Snoring, nasal voice, epistaxis, rhinorrhoea, local pain, dysphagia, cranial nerve palsies |
| Paranasal sinuses | Swelling, pain, sinusitis, obstruction, epistaxis, cranial nerve palsies |
| Middle ear | Chronic otitis media, haemorrhagic discharge, cranial nerve palsies, extruding polypoid mass |
| Larynx | Hoarseness, irritating cough |
| Trunk | Asymptomatic mass (usually) |
| Biliary tract | Hepatomegaly, jaundice |
| Retroperitoneum | Painless mass, ascites, gastrointestinal or urinary tract obstruction, spinal cord symptoms |
| Bladder/prostate | Haematuria, urinary retention, abdominal mass, constipation |
| Female genital tract | Polypoid vaginal extrusion of mucosanguineous tissue, vulval nodule |
| Male genital tract | Painful or painless scrotal mass |
| Extremity | Painless mass, may be very small but with secondary lymph node involvement |
| Metastatic | Non-specific symptoms, associated with the diagnosis of leukaemia |