Manifestations

Additional Manifestations

Weight/Score

Skin thickening of fingers of both hands extending proximal to MCPs

-

9

Skin thickening of fingers (count higher score only)

Puffy fingers

2

Sclerodactyly of fingers distal to the MCPs but proximal to PIPs

4

Fingertip lesions

Digital tip ulcers

2

Fingertip scars

3

Telangiectasia

-

2

Abnormal nailfold capillaries

-

2

Pulmonary hypertension and/or interstitial lung disease (maximum score is 2)

Pulmonary hypertension

2

Interstitial lung disease

2

Raynaud’s phenomenon

-

3

SSc-related autoantibodies (maximum score is 3)

Anticentromere

3

Anti-Scl 70 (Antitopoisomerase-1)

3

Anti-RNA polymerase III

3

The patient discussed in this case had a score of 16, hence the diagnosis of SSc was made