Characteristics

Number

Percentage

Consanguinity of parents

Yes

10

34

No

8

28

Not specified

11

38

Reason for consultation

Anemia

20

69

Deterioration of general condition

3

10.3

Epistaxis

3

10.3

Suspected leukemia

2

7

Abdominal pain

1

3.4

Syndromes found

Infectious syndrome

23

79

anemic syndrome

15

52

Hemorrhagic Syndrome

8

28

The three associated syndromes

8

28

Blood count abnormalities

Anemia

27

93.1

Thrombocytopenia

25

86.2

Leukopenia

20

69

Neutropenia

19

65.5

Lymphopenia

8

27.6

Monocytopenia

7

24.1

Specific treatment

Corticosteroid

17

58.6

Androgen

6

20.7

Immunosuppressive

6

20.7

becoming

alive

18

62

deceased

10

35

lost view

1

3