“Systemic” polygenic autoinflammatory diseases | Number | Pourcentage | ||
Systemic vascularitis non-autoimmune (n = 6 cases; 75.00% of cases) | Horton’s disease | 2 | 25.00 | |
Periartritis nodosa | 1 | 12.50 | ||
Vasculitis of undetermined origin | 1 | 12.50 | ||
Autres | Burger Angitis | 1 | 12.50 | |
Leukocytoclassical Vascularitis | 1 | 12.50 | ||
Systemic Sarcoidosis | 1 | 12.50 | ||
Still’s disease | 1 | 12.50 | ||
Total | 8 | 100.00 |