“Systemic” polygenic autoinflammatory diseases

Number

Pourcentage

Systemic vascularitis non-autoimmune

(n = 6 cases; 75.00% of cases)

Horton’s disease

2

25.00

Periartritis nodosa

1

12.50

Vasculitis of undetermined origin

1

12.50

Autres

Burger Angitis

1

12.50

Leukocytoclassical Vascularitis

1

12.50

Systemic Sarcoidosis

1

12.50

Still’s disease

1

12.50

Total

8

100.00