Homozygous sickle cell parents | None | 145 | 88.96 |
Both | 7 | 4.29 | |
Father | 7 | 4.29 | |
Mother | 4 | 2.45 | |
Sickle cell disease in siblings | Yes | 115 | 71.43 |
No | 44 | 27.33 | |
Not known | 2 | 1.24 | |
Age at disease diagnosis (in months) | [12 - 48] | 66 | 37.67 |
[60 - 108] | 32 | 18.49 | |
[120 - 168] | 32 | 18.49 | |
[6 - 11] | 25 | 14.38 | |
<6 | 10 | 6.16 | |
>168 | 8 | 4.79 | |
Number of hospitalizations during last 12 months | None | 61 | 36.97 |
1 time | 30 | 18.18 | |
>3 times | 29 | 17.58 | |
2 times | 23 | 13.94 | |
3 times | 22 | 13.33 | |
Common reason for hospitalizations | Vaso-occlusive crises | 104 | 70.27 |
Anemia | 50 | 33.78 | |
Infections | 25 | 16.89 | |
Number of vaso-occlusive crises during the last 12 months | >3 times | 64 | 42.67 |
None | 27 | 18.00 | |
1 time | 23 | 15.33 | |
2 times | 23 | 15.33 | |
3 times | 13 | 8.67 | |
Type of complications | Acute | 103 | 76.00 |
Chronic | 32 | 24.00 | |
Number of blood transfusions in the last 12 months | None | 25 | 64.10 |
>3 times | 8 | 20.51 | |
2 times | 5 | 12.82 | |
1 time | 1 | 2.56 | |
Taking hydroxyurea | No | 143 | 83.63 |
Yes | 28 | 16.37 |