Vomiting

Constipation

Diarrhea

Headache

49 (15.3%)

43 (13.4%)

20 (6.2%)

9 (2.8%)

Myalgia

Cutaneous manifestations

8 (2.5%)

30 (9.3%)

Buccal or genital aphthosis

18 (60%)

Erysipelas like rash

1 (3.3%)

Recurrent pruritic rash

4 (13.3%)

Angioedema or urticaria

1 (3.3%)

Cutaneous photosensitivity

6 (20%)

Episode attack

<1 attack per month

100 (31.2%)

1 - 2 attacks per month

131 (40.8%)

>2 attacks per month

90 (28%)

Duration

≤5 days

304 (94.7%)

>5 days

17 (5.3%)

Appendectomy

8 (2.5%)

Number of hospital admission before diagnosis

144 (44.9%)

1 - 3 hospitalization

127 (88.2%)

>3 hospitalization

17 (11.8%)

Disease severity score

Mild

Moderate

Severe

132 (41.1%)

187 (58.3%)

2 (0.6%)