Major Criteria

1. Recurrent febrile episodes accompanied by peritonitis, synovitis or pleuritis

2. Amyloidosis of the AA type without predisposing disease

3. Favorable response to continuous colchicine treatment

Minor Criteria

1. Recurrent febrile episodes

2. Erysipelas-like erythema

3. FMF in a first-degree relative

Definite diagnosis: 2 major or 1 major and 2 minor criteria

Probable diagnosis: 1 major and 1 minor criteria