Major Criteria |
1. Recurrent febrile episodes accompanied by peritonitis, synovitis or pleuritis 2. Amyloidosis of the AA type without predisposing disease 3. Favorable response to continuous colchicine treatment |
Minor Criteria |
1. Recurrent febrile episodes 2. Erysipelas-like erythema 3. FMF in a first-degree relative |
Definite diagnosis: 2 major or 1 major and 2 minor criteria Probable diagnosis: 1 major and 1 minor criteria |