| Major Criteria |
| 1. Recurrent febrile episodes accompanied by peritonitis, synovitis or pleuritis 2. Amyloidosis of the AA type without predisposing disease 3. Favorable response to continuous colchicine treatment |
| Minor Criteria |
| 1. Recurrent febrile episodes 2. Erysipelas-like erythema 3. FMF in a first-degree relative |
| Definite diagnosis: 2 major or 1 major and 2 minor criteria Probable diagnosis: 1 major and 1 minor criteria |