Characteristics (n = 92) |
|
Age (years), mean ± SD | 40.8 ± 12.8 |
Sex (male), n (%) | 50 (54.0) |
Age of onset (years) mean ± SD | 19.4 ± 8.9 |
Duration of the disease (years) mean ± SD | 21.8 ± 9.5 |
Family History (+/−) | 38/54 |
Mode of Inheritance |
|
Autosomal dominant | 8 (21) |
Autosomal recessive | 30 (79) |