Reference

Number of patients

Sex

CD^a

(age at diagnosis, years)

Location of CD^a

CD^a

(age at diagnosis, years)

Treatment of CD^a

Mortality for CCA^b

Disease duration

(years)

Location of tumor

Berman (1980)

1

F

30

Small bowel

43

N/A

N/A

13

Hilar

Krause (1985)

1

M

10

N/A

31

MT^d

N/A

21

N/A

Altaee (1991)

4

F

N/A

N/A

57±17

N/A

N/A

8.5

Hilar

Choi (1994)

1

F

27

N/A

57

N/A

YES

30

Hilar

Biancone (2006)

1

M

25

N/A

48

MT^d + AZA^e + IFX^f

YES

23

N/A

Present report (2013)

1

M

20

Right colon

30

AZA^e + IFX^f

YES

10

Intrahepatic

Summary

9

6F/3M

Range 10 - 48.5

-

Range 30 - 57

-

Range 10 - 30

-