Signs of organ(s) diffusely or partially enlarged, or in nodular form.

Serum IgG4 level > or equal to 1.35 g/l.

Histopathological examination: lymphoplasmacytic infiltrate with sclerosis IgG4+/IgG+ cell ratio > 40%, and > or equal to 10 IgG4+ plasma cells/HPF.

Confirmed diagnosis: 1 + 2 + 3; probable 1 + 3; possible 1 + 2 HPF: high power field.