SYSTEMIC DISEASES

NUMBER

SYSTEMIC

AUTOIMMUNE

DISEASES

Rheumatoid Arthritis

564

Systemic Lupus erythematosus

56

Sjögren’s syndrome

32

Systemic Sclerosis

26

Idiopathic

Inflammatory

Myopathy

Dermatomyositis

8

21

Polymyositis

4

Overlap myositis

8

Antisynthetase Syndrome

1

Undifferentiated connective tissue diseases

20

Mixed Connective tissue disease

6

Anti-phospholipids’ syndrome

6

Overlap Connective tissue disease

31

SYSTEMIC

VASCULITIS

GPA

3

19

PAN

1

Vasculitis associated with systemic diseases

6

Cryoglobinemic Vasculitis

1

Behçet’s disease

6

Takayasu Arteritis

2

SYSTEMIC

GRANULOMATOSIS

Systemic Sarcoidosis

8

11

GPA

3

OTHER SYSTEMIC

DISEASES

Adult-onset Still’s Disease

3

7

Amyloidosis associated with systemic diseases

2

Immune Defiencies with systemic manifestations

2