n (%), mean (SD) | |
Gender (% female) | 35 (52%) |
Age | 29 (8.9) |
Body Mass Index (kg/m2) | 23 (3.7) |
Ethnicity | |
Caucasian | 57 (84%) |
Hispanic | 9 (13%) |
African-American | 2 (3%) |
Medical History | |
Pulmonary Hypertension | 6 (9%) |
Cystic Fibrosis Related Diabetes | 38 (56%) |
Pneumothorax | 1 (2%) |
Lobectomy | 3 (4%) |
Genotype | |
F508del Homozygous | 26 (38%) |
F508del Heterozygous | 33 (49%) |
Other | 8 (12%) |
Mortality (% expired) | 13 (20%) |
Total exacerbations over 1 year | 0.7 (0.9) |
Total exacerbations over 3 years | 2.3 (2.5) |
CFQ-R-Respiratory Score (%) | 75 (15) |
Lung Function | |
FEV1 (% pred) | 61 (27) |
FVC (% pred) | 74 (20) |
FEV1/FVC (%) | 64 (15) |
TLC (% pred) | 102 (15) |
IC (% pred) | 90 (23) |
IC/TLC (%) | 43 (11) |
FRC (% pred) | 107 (31) |
FRC/TLC (%) | 57 (11) |
RV (% pred) | 176 (79) |
RV/TLC (%) | 43 (16) |