| n (%), mean (SD) | |
| Gender (% female) | 35 (52%) |
| Age | 29 (8.9) |
| Body Mass Index (kg/m2) | 23 (3.7) |
| Ethnicity | |
| Caucasian | 57 (84%) |
| Hispanic | 9 (13%) |
| African-American | 2 (3%) |
| Medical History | |
| Pulmonary Hypertension | 6 (9%) |
| Cystic Fibrosis Related Diabetes | 38 (56%) |
| Pneumothorax | 1 (2%) |
| Lobectomy | 3 (4%) |
| Genotype | |
| F508del Homozygous | 26 (38%) |
| F508del Heterozygous | 33 (49%) |
| Other | 8 (12%) |
| Mortality (% expired) | 13 (20%) |
| Total exacerbations over 1 year | 0.7 (0.9) |
| Total exacerbations over 3 years | 2.3 (2.5) |
| CFQ-R-Respiratory Score (%) | 75 (15) |
| Lung Function | |
| FEV1 (% pred) | 61 (27) |
| FVC (% pred) | 74 (20) |
| FEV1/FVC (%) | 64 (15) |
| TLC (% pred) | 102 (15) |
| IC (% pred) | 90 (23) |
| IC/TLC (%) | 43 (11) |
| FRC (% pred) | 107 (31) |
| FRC/TLC (%) | 57 (11) |
| RV (% pred) | 176 (79) |
| RV/TLC (%) | 43 (16) |