OI absent

OI present

p-value

Number

4

7

Age (years)

44 ± 3

27 ± 9

<0.05

Length (cm)

173 ± 8

170 ± 10

ns

Weight (kg)

65 ± 8

61 ± 11

ns

Disease duration (years)

9 (8 - 11)

7 (5.5 - 8.5)

ns

Blood volume per kg (ml)

66 ± 9

55 ± 4

<0.05

RBC volume per kg (ml)

23 ± 3

19 ± 1

<0.05

Plasma volume per kg (ml)

43 ± 6

37 ± 3

0.09

Percentage norm blood volume (%)

94 ± 10

77 ± 7

<0.02

Percentage norm RBC volume (%)

96 ± 10

76 ± 7

<0.01

Percentage norm RBC volume (%)

93 ± 10

77 ± 7

<0.05