Mimickers of systemic juvenile arthritis (and vice versa)

Examples

Infection

Ÿ Deep-seated infections: abscesses or osteomyelitis

Ÿ Prolonged fever causes: tuberculosis, brucellosis

Ÿ Post-infectious arthritis: streptococci

Ÿ Viruses: EBV, CMV, parvovirus, measles, HIV

Malignancy

Leukemia or lymphoma

Autoimmune disease

SLE or polyarticular JIA with systemic manifestations

Vasculitis

KD or polyarteritis nodosa

Autoinflammatory periodic fever diseases

TNF receptor periodic fever

Immunodeficiencies

Especially those that may present with HLH