Variables

Patients with ILD

(n = 102)

Patients without ILD

(n = 247)

p-value

Age (years)

69.9 ± 9.7

61.0 ± 12.9

<0.001

Gender (M/F)

55/47

110/137

0.110

MPO-positive AAV

99 (97.1%)

217 (87.9%)

0.008

PR3-positive AAV

3 (2.9%)

30 (12.2%)

General manifestation

69 (67.7%)

173 (70.0%)

0.659

Skin involvement

3 (2.9%)

19 (7.7%)

0.097

ENT involvement

5 (4.9%)

10 (4.1%)

0.946

Cardiovascular involvement

25 (24.5%)

87 (35.2%)

0.051

Abdominal involvement

27 (26.5%)

73 (29.6%)

0.562

Nervous system involvement

11 (10.8%)

28 (11.3%)

0.882

Kidney involvement

77 (75.5%)

210 (85.0%)

0.034

Hemoglobin (g/L)

94.5 (79.8, 116.3)

90.0 (74.0, 107.0)

0.105

Serum albumin (g/L)

31.0 (26.8, 35.3)

30.0 (26.0, 35.0)

0.293

Complement C3 (g/L)

0.77 (0.65, 0.93)

0.81 (0.66, 0.92)

0.245

Complement C4 (g/L)

0.24 (0.17, 0.29)

0.21 (0.17, 0.26)

0.109

BVAS

14.5 (10.0, 17.3)

15.0 (11.0, 18.0)

0.666

Survival

48 (48.9%)

137 (60.9%)

0.047

Death

50 (51.0%)

88 (39.1%)