Symptoms

Score

Epistaxis

0 = No or trivial

2 = Packing, cauterization

1 = Present

3 = Transfusion, replacement

Cutaneous symptoms

0 = No or trivial

2 = Hematomas

1 = Petechiae or bruises

3 = Medical consultation

Minor wounds

0 = No or trivial

2 = Medical consultation

1 = Present (1 - 5 episodes/year)

3 = Surgery/blood transfusion

Oral cavity bleeding

0 = No or trivial

2 = Medical attention

1 = Present

3 = Surgery/blood transfusion

Gastrointestinal bleeding

0 = No or trivial

2 = Medical Attention

1 = Present

3 = Surgery/blood transfusion

Muscle hematomas of hemarthrosis

0 = No or trivial

2 = Medical Attention

1 = Present

3 = Transfusion/intervention

Tooth extraction (most severe episode)

0 = No or trivial

2 = Suturing of packing

1 = Present

3 = Transfusion

Surgery (most severe episode)

0 = No or trivial

2 = Suturing or resurgery

1 = Present

3 = Transfusion

Menorrhagia

0 = No or trivial

2 = Consultation, pill use, iron therapy

1 = Present

3 = Transfusion, hysterectomy, dilatation-curettage, replacement therapy