Reference

Age/sexe

Localisation

Clinical presentation

Treatment

Metastasis ondiagnosis

Survival

Hori and Kato 2000 [15] .

40/M

Jejunum

Intestinal perforation

Surgery/CMT

ND

5

Sarangarajna, et al. 2001 [16] .

13/M

Jejunum

Occlusion

Surgery

Absent

12 NID

Shek, et al. 2001 [17] .

9/F

Small bowel

Abdominal distension

Surgery/CMT

Pelvis

25

Adair, et al. [7].

21/f

Duodenum

Surgery/CMT

ND

10 NID

Graham, et al. 2002 [18] .

14/M

Ileum

Anemia

Surgery/CMT

ND

52 NID

Balasubramanian, et al. 2002 [19] .

53/F

Ileum

Abdominal Mass

Surgery

ND

ND

Kie, et al. 2003 [20] .

20/F

Duodenum

ulcer

Surgery/CMT

18 NID

Boehm, et al. 2003 [21] .

18/M

Ileum

Occlusion

Surgery/CMT

Peritoneum

ND

Bala, et al. 2006 [22] .

57/F

Ileum

Mass

Surgery/CMT

ND

8 NID

Batzioui, et al. 2006 [23] .

66/M

Small bowel

Surgery/CMT

ND

48 NID

Kim, et al. 2007 [24] .

63/M

Ileum

Occlusion

Surgery/CMT

Lymph nodes

ND

Sethi and Smith 2007 [25] .

44/M

Ileum

Occlusion

Surgery/CMT

ND

13

Rodarte-Shade, et al. 2012 [26] .

32/M

Ileum

Anemia

Surgery/CMT

Absent

6 NID

Vignali, et al. 2012 [8] .

15/F

Ileum

Mass

Surgery/CMT

ND

ND

Prasertvit, Stoikes 2013 [27] .

28/F

Small bowel

ND

ND

ND

ND

Kim, et al. 2013 [28] .

23/M

Jejunum

Tumor rupture without perforation

Surgery/CMT

Liver and lymph nodes

ND

Rachan Shetty 2014 [29] .

24/M

Ileum

Occlusion

Surgery/CMT

ND

15 NID

Milione, et al. 2014 [30] .

18/M

Ileum

Liver metastasis

ND

Liver

8

Milione, et al. 2014 [30] .

20/M

Ileum

Liver metastasis

ND

Liver

28

Milione, et al. 2014 [30] .

42/M

Ileum

ND

Surgery/CMT

absent

11

Milione, et al. 2014 [30] .

45/M

Ileum

ND

Surgery/CMT

absent

13

Milione, et al. 2014 [30] .

15/F

Ileum

ND

Surgery CMT/RTH

absent

28

Milione, et al. 2014 [30] .

57/M

Ileum

ND

Surgery

absent

ND

Milione, et al. 2014 [30] .

28/F

Ileum

Surgery

Liver

204 NID

Padma, et al. 2015 [31] .

22/F

Jejunum

Mass

Surgery

absent

ND

Peng, et al. 2015 [32] .

59/M

Ileum

Abdominal pain

Surgery

ND

ND

Peng, et al. 2015 [32] .

22/M

Ileocecum

Mass

Surgery

Liver

ND

Peng, et al. 2015 [32] .

36/F

Ileocecum

Mass

Surgery/CMT

ND

34

Liu, et al. 2016 [33] .

15/M

Jejunum

Hematemesis, Melena, anemia

Surgery

ND

7

Li, et al. 2017 [34] .

16/F

Ileum

Anemia

Surgery

ND

10 NID

Kim, et al. 2017 [35] .

9/F

Jejunum

Anemia

Surgery/CMT

Peritoneum

ND

Liao, et al. 2018 [36] .

25/F

Ileum

Mass

Surgery

ND

ND

Cantu, et al. 2019 [37] .

67/F

Jejunum

Abdominal pain + constipation

Surgery

absent

3 NID.

Yagnik, et al. 2019 [38] .

42/M

Jejunum

perforation

Surgery/CMT

ND

9 NID

Andrej, et al. 2020 [39] .

30/F

Jejunum

asthenia

Surgery

absent

2

Our case

26/F

Ileum

Abdominal pain, transit disorder

Surgery/CMT

absent

No recurrence at 12 month.