|
| Frequency (%) |
| Early symptoms |
|
| PNS symptoms | 3/12 (25) |
| GI symptoms | 3/12 (25) |
| Dyshidrosis | 3/12 (25) |
| Angiokeratomas | 3/12 (25) |
| Hearingloss | 0/12 (0) |
| Cornea verticillata | 1/12 (8.33) |
| Pathological albuminuria | 2/12 (16.66) |
| Mayor complications |
|
| Cardiac | 0/12 (0) |
| Renal | 0/12 (0) |
| CNS | 0/12 (0) |