| Frequency (%) |
Early symptoms |
|
PNS symptoms | 3/12 (25) |
GI symptoms | 3/12 (25) |
Dyshidrosis | 3/12 (25) |
Angiokeratomas | 3/12 (25) |
Hearingloss | 0/12 (0) |
Cornea verticillata | 1/12 (8.33) |
Pathological albuminuria | 2/12 (16.66) |
Mayor complications |
|
Cardiac | 0/12 (0) |
Renal | 0/12 (0) |
CNS | 0/12 (0) |