Parameters

Age of presentation “months”

mean ± SD

Frequency of blood transfusion

Splenectomy

Hb

Hb F%

Regular (every 3 w)

Regular (every 5 w)

Yes

No

mean ± SD

mean ± SD

rs 9376090

TT

6.6 ± 1.4

34 (82.8%)

7 (7.2%)

33 (80.5%)

8 (19.5%)

7.8 ± 1.34

17.2 ± 15.0

CT

6.5 ± 1.2

2 (33.3%)

4 (66.6%)

4 (66.7%)

2 (33.3%)

7.3 ± 1.1

10.1 ± 7.5

CC

6.6 ± 1.1

1 (33.3%)

2 (66.6%)

2 (66.7%)

1 (33.3%)

6.5 ± 1.05

18.3 ± 16.5

P value

0.737

0.469

0.663

0.259

0.620

rs 4895441

AA

6.7 ± 1.4

22 (78.6%)

6 (21.4%)

21(75.0%)

7 (25.0%)

7.4 ± 0.96

17.8 ± 14.9

AG

6.5 ± 1.3

14 (70%)

6 (30%)

17 (85.0%)

3 (15.0%)

8.05 ± 1.7

14.3 ± 13.4

GG

7.0 ± 1.4

1 (50%)

1 (50%)

1 (50.0%)

1 (50.0%)

7.09 ± 0.57

17.5 ± 23.3

P Value

0.848

0.095

0.442

0.278

0.678