Parameters | SSFA2 phenotype—n (%) | SFA2 phenotype—n (%) | ||
Inclusion | M12 | Inclusion | M12 | |
Sleeping and eating disorders | 21 (63.6%) | 4 (13.8%) | 4 (66.7%) | 1 (16.7%) |
Joint and abdominal pains | 19 (57.6%) | 13 (44.8%) | 3 (50.0%) | 2 (33.3%) |
Hospitalization/transfusion | 26 (78.8%) | 1 (3.4%) | 4 (66.7%) | - |
Jaundice | 25 (75.8%) | 21 (72.4%) | 4 (66.7%) | 3 (50.0%) |
Liver damage | 4 (12.1%) | - | 1 (16.7%) | - |
Kidney damaged | 1 (3.0%) | 1 (3.4%) | 1 (16.7%) | - |
Spleen damaged | 18 (54.5%) | 2 (6.9%) | - | - |
Deaths | 4 (12.1%) | - | ||
HbF levels below 10% | 19 (57.6%) | 6 (20.7%) | 3 (50.0%) | - |
HbF levels (average ± SD %) | 9.0 ± 5.6 | 13.9 ± 7.2 | 17.6 ± 6.6 | 18.4 ± 6.8 |
Between 6 and 12 months age | 4 (12.1%) | - | ||
Between 13 and 24 months age | 7 (21.2%) | 1 (16.7%) | ||
More than 24 months age | 22 (66.7%) | 5 (66.7%) | ||
Hb (G/dL) | 6.9 ± 1.9 | 8.1 ± 1.6 | 6.7 ± 3.3 | 9.3 ± 1.0 |
Minimum-Maximum age | 5.1 - 8.5 | 5.4 - 13.2 | 6.6 - 8.4 | 7.8 - 10.0 |
Hypochromia | 17 (51.5%) | 13 (44.8%) | 3 (50.0%) | 3 (50.0%) |
Microcytosis | 9 (27.2%) | 6 (20.7%) | 2 (33.3%) | 4 (66.7%) |
White blood cells—WBC count (×103) | 12.8 ± 4.7 | 9.8 ± 3.1 | 12.5 ± 3.1 | 9.5 ± 2.1 |
Minimum-Maximum WBC count | 8.2 - 30.0 | 4.1 - 15.1 | 11.8 - 16.2 | 7.6 - 12.4 |
Platelets count (×105) | 371 ± 113 | 315 ± 109 | 400 ± 117 | 273 ± 95 |
Minimum-Maximum Platelet count | 252 - 679 | 145 - 609 | 381 - 438 | 151 - 354 |
Total | 33 | 30 | 6 | 5 |