Subject

Age (years)

Sex

Weight (kg)

Height (cm)

Height percentile for age and gender

BMIa,

Kg/m2

BMI percentile for age and gender

SBP/DBP

(mmHg)b

Serum

creatinine (mg/dL)c (µmol/l)

eGFRd

Proteinuria at:

Renal ultrasound

BPD/TD/CTe, cm

1st

screening

4th

screening

1

11

M

24.5

125.0

<3rd percentile

15.7

<25th percentile

100/60

0.66

(58.0)

104.2

1+

(30 mg/dL)

1+

(30 mg/dL)

Right kidney: 8.3/3.4/4.2

Left kidney: 8.2/3.6/4.1

Both kidneys are shrunken with preserved corticomedullary differentiation.

2

10

F

26.1

127.4

5th percentile

16.1

<50th percentile

110/50

NA

NA

1+

(30 mg/dL)

2+

(100 mg/dL)

NA

3

11

M

28.9

141.0

<50th percentile

14.6

<10th percentile

90/70

0.50 (44.0)

155.1

1+

(30 mg/dL)

2+

(100 mg/dL)

Right kidney: 9.0/3.1/6.1

Left kidney: 9.1/3.8/5.3

Both kidneys are shrunken with preserved corticomedullary differentiation.

4

11

F

25.5

143.4

<50th percentile

13.0

<3rd percentile

120/70

1.24 (110.0)

63.4

1+

(30 mg/dL)

2+

(100 mg/dL)

NA

5

13

F

36.6

147.1

<3rd percentile

16.6

<25th percentile

80/50

1.26

(111.0)

64.2

1+

(30 mg/dL)

1+

(30 mg/dL)

NA

6

11

F

27.8

133.2

<10th percentile

16.4

<50th percentile

90/60

0.65

(57.0)

113.6

3+

(500 mg/dL)

2+

(100 mg/dL)

Right kidney: 8.4/3.3/4.9

Left kidney: 8.6/4.4/5.5

Both kidneys are shrunken with preserved corticomedullary differentiation.