| Diagnosis | C1-INH | C1-INH function | C4 | C1q | Autoantibodies against C1-INH |
| HAE wit C1-INH deficiency | Low | Low | Low | Normal | Absent |
| HAE type 2 | Normal | Low | Low | Normal | Absent |
| AAE Type1 | Low | Low | Low | Low | Absent |
| AAE Type2 | Low/Normal | Low | Low | Low | Positive |