Parameter

Median

Range

Age (months)

98

1 - 204

Body weight (kg)

19.5

3.7 - 72

Underlying disease

Number (n)

Percent

Biliary atresia

20

51.3%

Alagille syndrome

5

12.8%

Polycystic kidney/liver disease

4

10.2%

Wilson’s disease

3

7.7%

Progressive intrahepatic cholestasis

2

5.1%

Acute liver failure of unknown origin

2

5.1%

Hepatoblastoma

1

2.6%

Hyperoxaluria type 2

1

2.6%

Niemann-Pick disease*

1

2.6%