| Author/Year | N˚ cases | Sex/Age (years) | Presentation | Histology | Treatment | Follow-up (months) |
| Carr et al. 1995 [17] | 13 | F (53%) 49 (22 - 92) | Acute appendicitis (30%) | Mucinous cystadenocarcinoma (46.1%)/Carcinoid (76%) | Not specified | OS 57 months: 100% (Only 7 patients followed) |
| Alsaad et al. 2009 [18] | 1 | F 46 | Acute right iliac fossa pain | Goblet cell carcinoma/Mucinous cystadenoma | Right colectomy | Not specified |
| Singh et al. [19] 2010 | 1 | M 52 | Chronic pain in right lower quadrant, palpable mass | Carcinoid/Mucinous adenocarcinoma | Right colectomy + omental deposit excision/Adjuvant ChT (6 months) | DFS 6 months: Peritoneal carcinomatosis, liver, omentum and rectus muscle metastases. OS: 14 months |
| Dellaportas et al. [20] 2014 | 1 | F 57 | Mass in right iliac fossa | Well-differentiated NET/mucinous cystadenoma | Laparoscopic appendectomy and right oophorectomy + complementary right colectomy | DFS 12 months |
| Villa et al. [21] 2021
| 10 | F (63.6%) 37.8 (23 - 60) | Acute appendicitis (63.6%) | LAMN/ANET | Appendectomy (90%)/Complementary right colectomy (63.6%)/CRS + HIPEC (45.5%) | DFS 18.5 months (6 - 60) 1 (9.09%) perihepatic and pleural recurrence |
| Ruiz et al. [22] 2021 | 1 | M 54 | Acute right iliac fossa pain | LAMN/well-differentiated ANET | Laparoscopic appendectomy and partial cecectomy | Not specified |
| Melendez, Esquivel et al. 2022 | 2 | F 82 | Acute right iliac fossa pain | Goblet cell adenocarcinoma/LAMN | Laparoscopic appendectomy/ Complementary right colectomy + CRS + HIPEC/Adjuvant ChT (6 months) | Starting surveillance |
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| M 41 | Acute right iliac fossa pain | Goblet cell adenocarcinoma/LAMN | Laparoscopic appendectomy | DFS 6 months |