Manifestations | Additional Manifestations | Weight/Score |
Skin thickening of fingers of both hands extending proximal to MCPs | - | 9 |
Skin thickening of fingers (count higher score only) | Puffy fingers | 2 |
Sclerodactyly of fingers distal to the MCPs but proximal to PIPs | 4 | |
Fingertip lesions | Digital tip ulcers | 2 |
Fingertip scars | 3 | |
Telangiectasia | - | 2 |
Abnormal nailfold capillaries | - | 2 |
Pulmonary hypertension and/or interstitial lung disease (maximum score is 2) | Pulmonary hypertension | 2 |
Interstitial lung disease | 2 | |
Raynaud’s phenomenon | - | 3 |
SSc-related autoantibodies (maximum score is 3) | Anticentromere | 3 |
Anti-Scl 70 (Antitopoisomerase-1) | 3 | |
Anti-RNA polymerase III | 3 | |
The patient discussed in this case had a score of 16, hence the diagnosis of SSc was made |