Type of vasculitis | Included vasculitis |
Large vessel vasculitis (LVV) | Takayasu arteritis (TAK) Giant cell arteritis (GCA) |
Medium vessel vasculitis (MVV) | Polyarteritis nodosa (PAN) Kawasaki disease (KD) |
Small vessel vasculitis (SVV) | Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) Microscopic polyangiitis (MPA) Granulomatosis with polyangiitis (Wegener’s) (GPA) Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA) Immune complex SVV Anti-glomerular basement membrane (anti-GBM) disease Cryoglobulinemic vasculitis (CV) IgA vasculitis (Henoch-Schönlein) (IgAV) Hypocomplementemic urticarial vasculitis (HUV) (anti-C1q vasculitis) |
Variable vessel vasculitis (VVV) | Behcet’s disease (BD) Cogan’s syndrome (CS) |
Single-organ vasculitis (SOV) | Cutaneous leukocytoclastic angiitis Cutaneous arteritis Primary central nervous system vasculitis Isolated aortitis Others |
Vasculitis associated with systemic disease | Lupus vasculitis Rheumatoid vasculitis Sarcoid vasculitis Others |
Vasculitis associated with probable etiology | Hepatitis C virus-associated cryoglobulinemic vasculitis Hepatitis B virus-associated vasculitis Syphilis-associated aortitis Drug-associated immune complex vasculitis Drug-associated ANCA-associated vasculitis Cancer-associated vasculitis Others |