Parameters

Values

Sporadic

Familial

Systemic involvement No. (%)

Musculoskeletal*

27 (79.41)

12 (92.31)

Constitutional

4 (11.76)

3 (23.08)

Skin

25 (73.53)

9 (69.23)

Discoid

8 (23.53)

2 (15.38)

Gastrointestinal§

3 (8.82)

1 (7.69)

Renal**

19 (55.88)

8 (61.54)

Haematological††

22 (64.71)

9 (69.23)

Cardiac‡‡

1 (2.94)

1 (7.69)

CNS§§

10 (29.41)

7 (53.85)

Pulmonary***

3 (8.82)

0 (0)

Onset age (mean ± SD) years

21.6 ± 5

22.1 ± 5.95

Number of ward admissions (mean ± SD)†††

1.3 ± 4.07

0.5 ± 0.44

Number of ICU admissions (mean ± SD)‡‡‡

0.1 ± 0.35

0 ± 0.02