Parameters | Values | ||
Sporadic | Familial | ||
Systemic involvement No. (%) | Musculoskeletal* | 27 (79.41) | 12 (92.31) |
Constitutional† | 4 (11.76) | 3 (23.08) | |
Skin‡ | 25 (73.53) | 9 (69.23) | |
Discoid | 8 (23.53) | 2 (15.38) | |
Gastrointestinal§ | 3 (8.82) | 1 (7.69) | |
Renal** | 19 (55.88) | 8 (61.54) | |
Haematological†† | 22 (64.71) | 9 (69.23) | |
Cardiac‡‡ | 1 (2.94) | 1 (7.69) | |
CNS§§ | 10 (29.41) | 7 (53.85) | |
Pulmonary*** | 3 (8.82) | 0 (0) | |
Onset age (mean ± SD) years | 21.6 ± 5 | 22.1 ± 5.95 | |
Number of ward admissions (mean ± SD)††† | 1.3 ± 4.07 | 0.5 ± 0.44 | |
Number of ICU admissions (mean ± SD)‡‡‡ | 0.1 ± 0.35 | 0 ± 0.02 |