Variables

MPO-positive (n = 316)

PR3-positive (n = 33)

p-value

Age (years)

Gender (M/F)

Variants of AAV

MPA

GPA

EGPA

General manifestation

Skin involvement

ENT involvement

Cardiovascular involvement

Abdominal involvement

Nervous system involvement

Pulmonary involvement

Alveolar hemorrhage

Interstitial lung disease

Kidney involvement

Proteinuria and/or Hematuria

SCR (μmol/L)

Hemoglobin (g/L)

Serum albumin (g/L)

Complement C3 (g/L)

Complement C4 (g/L)

BVAS

Survival

Death

64.4 ± 12.2

148/168

238 (75.3%)

63 (19.9%)

15 (4.8%)

220 (69.6%)

17 (5.4%)

14 (4.4%)

105 (33.2%)

90 (28.5%)

37 (11.7%)

154 (48.7%)

44 (13.9%)

99 (31.3%)

262 (82.9%)

237 (75.0%)

239 (80.5, 602.5)

90.5 (75.0, 108.0)

30.0 (26.0, 35.0)

0.79 (0.66,0.93)

0.22 (0.17,0.27)

15.0 (11.0,18.0)

168 (57.5%)

124 (42.5%)

56.4 ± 15.4

17/16

20 (60.6%)

11 (33.3%)

2 (6.1%)

22 (66.7%)

5 (15.2%)

1 (3.0%)

7 (21.2%)

10 (30.3%)

2 (6.1%)

10 (30.3%)

4 (12.1%)

3 (9.1%)

25 (75.8%)

21 (63.6%)

145 (68.0, 474.5)

97.0 (84.0, 120.5)

31.0 (25.0, 36.0)

0.80 (0.62, 1.00)

0.23 (0.19, 0.29)

15.0 (9.0, 17.5)

17 (54.8%)

14 (45.2%)

0.007

0.608

0.173

0.726

0.069

1.000

0.159

0.826

0.490

0.044

0.984

0.008

0.306

0.157

0.153

0.134

0.895

0.883

0.368

0.663

0.773