Signs | Frequency (n) | Percentage (%) |
Motor signs |
|
|
Myoclonus | 14 | 9 |
Tremor | 39 | 24.8 |
Asterixis | 7 | 4.5 |
Fasciculations | 3 | 1.9 |
Muscle tone abnormalities |
|
|
Spastic hypertonia | 2 | 1.3 |
Plastic hypertonia | 4 | 2.5 |
Hypotonia | 2 | 1.3 |
Reflex jerk of the lower limbs |
|
|
Hyporeflexia/areflexia | 76 | 48.4 |
Hyperreflexia | 5 | 3.2 |
Sensitivity abnormality |
|
|
Monofilament perception |
|
|
Reduced | 46 | 44.58 |
Absent | 16 | 11.94 |
Perception test on diapason |
|
|
Reduced | 50 | 43.3 |
Absent | 17 | 12.69 |
Cranial nerve involvement |
|
|
Nerve I | 5 | 3.2 |
Nerve VII | 6 | 3.8 |
Nerve VIII | 14 | 8.9 |
Orthostatic disturbances |
|
|
Orthostatic hypotension | 25 | 15.9 |
Orthostatic vertigo | 21 | 13.4 |
Other syndromes |
|
|
Pyramidal syndrome | 10 | 6.4 |
Cerebellar syndrome | 4 | 2.5 |
Spinal cord compression | 1 | 0.6 |