Type

Description

1

Partial quantitative deficiency of vWF

2

Qualitative defects of vWF

2A

Decreased vWF-dependent platelet adhesion and absence of vWF polymers

2B

Increased binding affinity of vWF for platelets

2M

Decreased vWF-dependent platelet adhesion; presence of vWF polymers

2N

Markedly decreased binding affinity of vWF for factor VIII

3

Virtually complete deficiency of vWF